RECENT CFTR AND CYSTIC FIBROSIS
REVIEWS
2001 "Cystic fibrosis: a brief look at
some highlights of a decade of research focused on elucidating and correcting
the molecular basis of the disease." Ko, YH., Pedersen,
PL J Bioenerg Biomembr. 2001
Dec;33(6):513-21. Also in this issue: "Overview: ABC
transporters and human disease." Gottesman, MM., Ambudkar,
SV J Bioenerg Biomembr. 2001 Dec;33(6):453-8.
2001 "CFTR: Interacting With
Everything?" Karl Kunzelmann News Physiol.
Sci. Vol 16 8/2001
2001 "A Combined Analysis of the Cystic Fibrosis Transmembrane Conductance Regulator: Implications for Structure and Disease Models" Chen, Jian-Min et al. Mol. Biol. Evol. 18(9):1771-1788 2001
2001 Minireview: "Regulation of the Cystic Fibrosis Transmembrane Conductance Regulator Cl- Channel by Its R Domain" Lynda S. Ostedgaard, Olafur Baldursson, and Michael J. Welsh J.Bio.Chem 3/16/01 Vol.276(11) pgs 7689-92
2001 "Cystic fibrosis: review of the decade"
Jaffe A, Bush A. Monaldi Arch Chest Dis 2001
Jun;56(3):240-7
2000 "Permeation Through the CFTR Chloride Channel" Nael A. McCarty. Journal of Experimental Biology 203: 1947-1962 2000
2000 "New Paradigms of CFTR Chloride Channel Regulation" K.L. Kirk; Cellular and Molecular Life Sciences Vol 57: 623-634
1999 Physiological Reviews (Supplement to:) 79:1 January 1999 ISSN 0031-9333 Editor: Raymond A. Frizzell This single supplement contains 11 review articles concerning CFTR and cystic fibrosis. These are as follows: "Ten Years With CFTR" Frizzell, pg S1-2, "Physological Basis of Cystic Fibrosis: A Historical Perspective", Quinton, pg S3-22, "Structure and Function of CFTR Chloride Channel" Sheppard and Welsh, S23-46, "CFTR: Mechanism of Anion Conduction" Dawson, Smith, Mansoura S47-76 "Control of CFTR Channel Gating by Phosphorylation and Nucleotide Hydrolysis" Gadsby and Nairn, S77-108, "Pharmacology of CFTR Chloride Channel Activity" Shultz, Singh, Devor, Bridges S109-144 "CFTR is a Conductance Regulator As Well As a Chloride Channel" Schwiebert, Benos, Egan, Stutts, Guggino S145-166 "Biosynthesis and Degredation of CFTR" Kopito S167-174 "Intracellular CFTR: Localization and Function" Bradbury S175-192 "Pathophysiology of Gene-Targeted Mouse Models for Cystic Fibrosis" Grubb, Boucher S193-214 "Role of CFTR in Airway Disease" Pilewski, Frizzell S215-255
1999 "Structure and Function of the Cystic Fibrosis Transmembrane Conductance Regulator" M.M. Morales, M.A.M Capella, A.G. Lopes Brazilian Journal of Medical and Biological Research (1999) 32: 1021-1028
1998 "The Cystic Fibrosis Transmembrane Conductance Regulator and its Function in Epithelial Transport" K. Kunzelmann Rev Physiol Biochem Pharmacol. 1999;137:1-70. Review.
1998 "What We Know and What We Do Not Know About Cystic Fibrosis Transmembrane Conductance Regulator" Jianjie Ma and Pamela B. Davis Clinics in Chest Medicine September, 1998 Vol 19, n(3): pgs 459-471
1998 "New Developments in Cystic Fibrosis" Valera L. Hudson and Margaret Guill Pediatric Annals 27:8 August 1998, pgs 515-520
1997 "Cystic Fibrosis: Channel, Catalytic, and Folding Properties of the CFTR Protein" Seibert, Loo, Clarke, Riordan. Journal of Bioenergetics and Biomembranes, 1997 Vol 29 n(5): 429-442
1997 "The Biogenesis, Traffic, and Function of the Cystic Fibrosis Transmembrane Conductance Regulator" Tamas Jiling and Kevin L. Kirk International Review of Cytology Vol 172 pgs 193-241
1996 "Understanding How Cystic Fibrosis Mutations Cause a Loss of Chloride Channel Function" David N. Sheppard and Lynda S. Ostedgaard Molecular Medicine Today July 1996: 290-297
For an excellent and broad overview of ion channel history and ion channel theory, we recommend Bertil Hille's book "Ionic Channels of Excitable Membranes" second edition, publisher: Sinauer Associates, Inc., 1992. ISBN # is 0-87893-323-9